Metabolomic Insights into the Nutritional Status of Adults and Adolescents with Phenylketonuria Consuming a Low-Phenylalanine Diet in Combination with Amino Acid and Glycomacropeptide Medical Foods

Figure 2

Caloric contribution from carbohydrate, sugar, protein, fat, and saturated fat was calculated for the low-Phe diet in combination with AA-MF as a percentage of total energy intake (a). Macronutrient distribution was similar for GMP-MF (data not shown). Caloric contribution from macronutrients was compared to the age-appropriate AMDR (protein, carbohydrate, and fat) or the DGA (sugar and saturated fat) (b) for each participant to determine the percentage of subjects that were below or above the AMDR or DGA (c). Percentage of participants with inadequate and excessive macronutrient distributions were similar for GMP-MF (data not shown). AA-MF, amino acid medical food; AMDR, acceptable macronutrient distribution ranges; DGA, Dietary Guidelines for Americans; GMP-MF, glycomacropeptide medical foods; Sat. fat, saturated fat.

(a)

(b)

(c)