Research Article
Clinical Course and Nutritional Management of Propionic and Methylmalonic Acidemias
Table 3
Observed daily protein intake.
| Age group | Number | Protein intake (gm/kg/day) | PROP recommendation (gm/kg/day) | Intact | Synthetic | Intact (%) | Total | Intact | Total |
| 0–6 months | 1 | 0.6 | 1.4 | 30 | 2 | 0.91–1.52 | 1.52–1.82 | 1–3 years | 5 | 0.7 ± 0.07 | 1.35 ± 0.13 | 34 ± 3.5 | 2.05 ± 0.11 | 0.63–1.05 | 1.05–1.26 | 4–8 years | 14 | 0.75 ± 0.1 | 1.38 ± 0.28 | 36 ± 6.3 | 2.12 ± 0.28 | 0.57–0.95 | 0.95–1.14 |
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