Review Article

Pulmonary Epithelial-Myoepithelial Carcinoma

Table 1

Clinical data of P-EMC cases.

Ref.Age (y)/SexSize (cm)LocationSmokingObstructive
symptoms
Immunohistochemical data
Inner cellOuter cell

[5]Average 55.5 (54-57)/M (1), F (3)Median 1.5
(1.5-5.0)
ENA+(3) NA (1)EMA(+); MNF116(+); and CD34(-)S-100(+); SMA(+); and vim(+)
[6]51/F3.3PNA-EMA(+); TTF-1(+)S-100(+); actin(+)
[7]76/F2.7P, UNA-CK(+); EMA(+); CEA(+); and TTF-1(+)S-100(+); actin(+); P63(+); CD10(+); and P27/kip-1(+)
[9]7/M3.6E--CK(+); AE1/3(+); and S-100(-)S-100(+); SMA(+)
[11]54/F1.5E+-CK7(+)S-100(+); SMA(+); P63(+); and CK5/6(+)
[12]Average 56.6 (52-62)/M (0), F (5)Median 1.2
(0.6-2.6)
PNA+(1) -(4)EMA(+); CK7(+); CK20(-); SPA(+); CAM5.2(+); and TTF-1(+)S-100(+); SMA(+); CK(+); P63(+); and calponin (+)
[13]Average 49.6 (38-56)/M (3), F (2)Median 3
(2.5-5)
ENA-CK(+); S-100(-); and SMA(-)S-100(+); SMA(+); CK(+); CD117(+); and GFAP(+)
[14]81/M0.4ENA-CK(+)S-100(+); P63(+); TTF-1(-); MIB-1(10%); and p27/kip-1(+)
[15]Average 60.4 (52-66)/M (3), F (2)Median 1.8
(0.7-12)
E+(3)+(4) -(1)CK(+); TTF-1(+)S-100(+); S-100(-); SMA(+); and P27(+)
[16]53/F2.2E-+CK(+)S-100(+); SMA(+)
[17]Average 52.5 (35-69)/M (2), F (6)Median 2.5
(2.0-16.0)
E (5), P, U (3)NA+CAM5.2(+); S-100(+); and CK(+)HHF35(+); S-100(+)
[18]55/F2.0E++CK(+); CAM5.2(+)S-100(+); SMA(+); vim(+); and GFAP(+)
[19]66/M16E+NACEA(+); EMA(+); and AE3(+)S-100(+); SMA(-); AE3(+/-); and GFAP(+)
[20]55/F3.9E-+CK(+); GEAP(-)S-100(+); SMA(+); and GFAP(-)
[21]47/FNAE-+CK(+); SMA(-)S-100(-); SMA(+);
CK(+); and vim(+)
[22]67/M1.3E++CAM5.2(+); AE1/3(+)S-100(+); SMA(+)
[23]73/M4.5E++EMA(+); CK(+); S-100(-); and vim(-)S-100(+); SMA(+); and vim(+)
[24]73/M3.8E++CK(+); EMA(+); and P53(+)S-100(+); SMA(+); GFAP(+); and P53(+)
[25]35/F13.0ENA+SMA(+); CD10(+)S-100(+); SMA(+); CD10(+); and GFAP(+)
[26]43/FNAE-+CK7(+); EMA(+); P53(+); and CD117(+)S-100(+); SMA(+); P53(+); and CD117(+)
[27]74/M1.5E++S-100(+); SMA(+); and vim(+)S-100(+); vim(+)
[28]Average 57/M (1), F (1)Median 6.9NANANANANA
[29]57/M2.0E+-CAM5.2(+); AE1/AE3(+); CK7(+); and CK903(+)S-100(+); SMA(+); GFAP(+); calponin(+); CD117(+); and P27/kip1(+)
[30]Average 63 (36-75)/M (3), F (4)Median 2.5
(1.3-4.0)
NANA+(3)NANA
[31]34/M1.15ENA+CK7(+); CK8/18(+)S-100(+); SMA(+); and P63(+)
[32]72/F3.8E--AE1/AE3(+)SMA(+); P63(+)
[33]58/M1.3P, U--CK(+); CEA(+); and TTF-1(+)S-100(+); CD10(+); P63(+); and P40(+)
[34]58/F1.5ENA-CK7(+)S-100(+); SMA(+); and P63(+)
[35]83/F8.3E++CK(+); TTF-1(-)S-100(+); actin(+); vim(+); and TTF-1(-)
[36]72/M3.5UNA-NANA
[37]50/F3.5E-+CK7(+); TTF-1(-)S-100(+); SMA(+); P40(+); and TTF-1(-)
[38]45/F5.4E-+CK(+); AB(+); and TTF-1(-);S-100(+); SMA(+); and PAS(-)
[39]55/M1.9E++AE1/AE3(+); CD117(+)S-100(+); SMA(-); P40(+); and P63(+)
[40]30/FNAENA+NANA
[41]76/F2.7ENA+CK(+); vim(-)S-100(+); P63(+); HHF(+); and CK(+)
[42]70/F5.0E++CK7(+); CD117(+); CK8(+); and TTF(-)S-100(+); SMA(+); CK5/6(+); P63(+); and P40(+)

M: male (number of people), F: female (number of people), NA: not available, E: endobronchial, P: pulmonary parenchyma, U: unrelated to the bronchial, CK: cytokeratin, EMA: epithelial membrane antigen, SMA: smooth muscle actin, GFAP: glial fibrillary acidic protein, vim: vimentin, SPA: surfactant proteins A, and TTF-1: thyroid transcription factor-1.