Clinical Features and Genetic Background of the Periodic Fever Syndrome with Aphthous Stomatitis, Pharyngitis, and Adenitis: A Single Center Longitudinal Study of 81 Patients

Table 1

Demographic and clinical characteristics of PFAPA patients.

Total number of patients	81
Male	50 (63%)
Female	31 (37%)
Age at disease onset (mean ± SD, range)	2.1 ± 1.5 years (0.1–6.5 years)
Age at diagnosis (mean ± SD, range)	3.9 ± 1.7 years (1.2–7 years)
Interval between disease onset and diagnosis (mean ± SD, range)	1.9 ± 1.5 years (0.4–6.5 years)
Duration of febrile episode (mean, range)	4.2 days (2–11 days)
Interval between episodes (mean, range)	4 weeks (14–60 days)