Research Article

Clinical Features and Genetic Background of the Periodic Fever Syndrome with Aphthous Stomatitis, Pharyngitis, and Adenitis: A Single Center Longitudinal Study of 81 Patients

Table 2

Signs and symptoms present in 81 PFAPA patients.

Symptom (%)

Adenitis76 (94%)
Pharyngitis79 (98%)
Aphthous stomatitis45 (56%)

Abdominal pain41 (51%)
Joint pain25 (31%)
Vomiting33 (41%)
Diarrhea18 (22%)
Skin rash10 (12%)