Research Article
Assessment of Selected Parameters of Liver Fibrosis and Inflammation in Patients with Diagnosed Cystic Fibrosis
Table 1
Clinical picture of the examined patients.
| | Values |
| | Age (years) | 9.8 (range: up to 1 year–20 years) | | Sex female/male () | 49/30 | | Mutation ( (%)) | | | delF508del/delF508del | 41/79 (51.9%) | | delF508del/other | 32/79 (40.5%) | | Other | 6/79 (7.6%) | | Shwachman-Kulczycki score (pts) | 75.56 (range 50-110) | | Clinical features ( (%)) | | | Pancreatic insufficiency | 69/79 (87.34%) | | Symptoms from the respiratory tract/recurrent respiratory tract infection | 64/79 (81%) | | Malnutrition (, taking into account age, sex, and population and laboratory test including albumin, total protein level) | 42/79% (53.2%) | | Liver dysfunction | 31/79 (39.2%) | | Salt loss syndrome | 9/79 (11.4%) | | History of meconium ileus/treated surgically | 4/79 (5.1%) |
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