Figure 2: Audiometric features of affected individuals III1, III2, III3, III4, and II7 at age of 19–53 years. Pure tone hearing thresholds were shown as the averages of the left and right sides. The rest of the four affected individuals I2 (80 y.o.), II1 (56 y.o.), II3 (55 y.o.), and II5 (59 y.o.) had hearing thresholds of 90 dB or higher.