Hearing Phenotypes of Patients with Hearing Loss Homozygous for the GJB2 c.235delc Mutation

Table 4

Audiogram shapes in patients with asymmetric and symmetric interaural HL.

Audiogram shape		The other ear
		Descending	Flat	Residual	Valley like	Ascending	Total deafness	Other
One ear	Descending	41 (9)	0 (21)	0 (8)	0 (6)	0 (1)	0 (2)	0 (13)
	Flat		16 (5)	0 (12)	0 (8)	0 (4)	0 (3)	0 (29)
	Residual			19 (0)	0 (1)	0 (0)	0 (5)	0 (12)
	Valley like				1 (0)	0 (1)	0 (1)	0 (7)
	Ascending					0 (1)	0 (0)	0 (2)
	Total deafness						6 (0)	0 (4)
	Other							5 (1)

(1) The value outside/inside each pair of parentheses represents the number of patients with symmetric/asymmetric interaural HL. (2) Italics indicate patients with the same audiogram shape for both ears.