Review Article

Practical Guidelines: Lung Transplantation in Patients with Cystic Fibrosis

Table 1

Preparatory tests for LTX*.

(i) Lab tests with blood group, HLA typing, and anti-HLA antibodies
(ii) Assessment of vaccination status, booster injection if necessary
(iii) Pulmonary function tests: body plethysmography, measurement of diffusion capacity, and standardised exercise test
(iv) Chest CT without contrast agent, preferably not older than 6 months
(v) Blood gas analysis at rest
(vi) Current sputum culture
(vii) ECG, echocardiography with evaluation of pulmonary artery pressure, and right ventricular function
(viii) Right heart catheter if necessary
(ix) Assessment of nutritional status
(x) Abdominal sonography (including recording signs of portal hypertension), abdominal CT if necessary
(xi) Gastroscopy and colonoscopy if necessary
(xii) ENT examination, with sinus CT scan if necessary, throat and sinus swabs if necessary
(xiii) Bone density scan
(xiv) Gynaecological/urologic screening
(xv) Psychological assessment
(xvi) Dental examination
(xvii) Presentation at ophthalmologist
(xviii) Presentation at dermatologist
(xix) Duplex sonography of the afferent arteries if necessary
(xx) Peripheral closing pressure of the ankle arteries if necessary

Listing reflects consensus of the ECORN-CF working group. Some centres may request further investigations.