Review Article

Pure Red Cell Aplasia and Lymphoproliferative Disorders: An Infrequent Association

Table 2

Histologic subtypes of lymphoid malignancies in association with PRCA [3, 4, 714]. Literature review was performed in references [4, 7, 11, 12] and the additional cases have been added to the Table.

Histologic subtype of lymphoproliferative disorderNumber of Cases (61 Total)References

Diffuse large B-cell lymphoma (DLBCL)8Hirokawa et al., 6 cases, 2009 [7], Sung et al., 1 case, 2007 [8], Suzuki et al., 1 case, 2007 [9]
Hodgkin’s disease4Hirokawa et al., 4 cases, 2009 [7]
Small lymphocytic lymphoma (SLL)1Vlachaki et al., 1 case, 2008 [3]
B chronic lymphocytic leukaemia (B-CLL)7Castelli et al., 1 case, 2002 [10] Narra et al., 6 cases, 2006 [11]
Nodal marginal zone lymphoma (NMZL)1Hirokawa et al., 1 case, 2009 [7],
Splenic marginal zone lymphoma (SMZL)3Narra et al., 1 case, 2006 [11], Anastasiadis et al., 2 cases, 2009 [4]
Mycosis fungoides1Hirokawa et al., 1 case, 2009 [7]
Angioimmunoblastic T-cell lymphoma (AITL)12Hirokawa et al., 4 cases, 2009 [7], Choi et al., 8 cases, 2010 [12]
Follicular lymphoma (FL)7Hirokawa et al., 6 cases, 2009 [7], Kuramoto et al., 1 case, 1998 [13]
Precursor T-lymphoblastic lymphoma (T-LBL)1Hirokawa et al., 1 case, 2009 [7]
Adult T-cell leukaemia/lymphoma (ATLL)1Hirokawa et al., 1 case, 2009 [7]
T-cell large granular lymphocyte (T-LGL) leukaemia15Go et al., 15 cases, 2001 [14]