Body Composition, Muscle Strength, and Physical Function of Patients with Bethlem Myopathy and Ullrich Congenital Muscular Dystrophy

Table 1

Body mass, adiposity, and muscularity. Summaries of individual data grouped according to sex.

Variable	Women (𝑛=5)	Men (𝑛=3)
Total mass (kg)	66.7±12.1; (range: 45–74)	66.3±11.1; (range: 55–77)
BMI (kg/m^2)	22.9±4.2; (range: 18–29)	22.3±3.6; (range: 18–26)
% FM	51.6±6.6; (range: 41–59)	34.6±14.2; (range: 18–44)
FMI (kg/m^2)	12.0±3.6; (range: 7–17)	8.0±4.0; (range: 3–11)
FFMI (kg/m^2)	10.9±0.8; (range: 10–12)	14.3±1.3; (range: 13–15)
AFFMI (kg/m^2)	4.2±0.8; (range: 3–5)	5.8±0.6; (range: 5–6)

BMI: body mass index, FM: fat mass, FMI: fat mass index, FFMI: fat free mass index, AFFMI: appendicular fat free mass index.