Body Composition, Muscle Strength, and Physical Function of Patients with Bethlem Myopathy and Ullrich Congenital Muscular Dystrophy

Table 5

Linear models (𝑦_𝑖=𝛽𝑥_𝑖+𝑒_𝑖) of separate relative contribution of body mass and muscularity to muscle strength and physical function.

Dependent variables	Predictor variables	𝛽	𝑅^2
Megascore (N)	BMI	27.22	0.81
	AFFMI	141.05	0.94
Hand grip (N)	BMI	2.82	0.77
	AFFMI	14.64	0.91
6MWD (m)	BMI	15.52	0.82
	AFFMI	77.58	0.90
% FVC	BMI	2.50	0.85
	AFFMI	12.48	0.93

𝑅²: coefficient of determination, 6MWD: 6 minute walking distance, N: Newton, FVC: forced vital capacity.