Clinical Study

Desmoplastic Small Round Cell Tumor of the Abdomen and Pelvis: Clinicopathological Characters of 12 Cases

Table 1

Clinical and CT characteristics of abdominal DSRCT.

Number Sex/age (years)Symptoms/signsTumor localization Treatment modalitySurvival and outcome (months)

1F/18 Palpable abdominal mass, distentionMesentery pelvic cavityBiopsy, chemotherapy7
2M/14Pain, vomiting palpable massOmentum mesentery pelvicBiopsy, chemotherapy9
3 M/23Abdominal pain, urinary retention Colon, pelvic concurrent metastasisBiopsy, chemotherapy11
4M/18 Vomiting, palpable massMesentery, abdomen, involving liver.Biopsy, chemotherapy11
5 M/38 Abdominal pain distentionMesentery, intestinesBiopsy, chemotherapy12
6M/54 VomitingIntestines, mesenteryUnresectable, chemotherapy37
7 F/18 Abdominal pain, palpable massRetroperitoneum, abdomenMultiple-organ en bloc resection chemotherapy13
8F/16 VomitingOmental and serosal surfaces Surgery complete chemotherapy 22
9M/24Nausea, palpable massIntestines, pelvis, and retroperitoneum Debulking surgery, chemotherapy24
10F/26 Abdominal distentionAbdomen, retroperitoneum Surgery (microresiduals), chemotherapy36
11M/21 Abdominal pain, hydronephrosisWidespread abdomen, peritoneumCytoreductive surgery, chemotherapy40
12M/39 No symptomOmentumComplete resection, chemotherapyFollowup 36, no evidence of disease

F: female, M: male.