Echocardiographic parameter (EP) Total (
, 100%) Exitus letalis = yes (
, 7.73%) Exitus letalis = no (
, 92.27%)
TT (kg) median (25–75) percentile 82.00 (73.00–93.00) 78.50 (65.00–80.00)
82.00 (73.00–93.00) 0.212 TV (cm) median (25–75) percentile 173.00 (165.00–180.00) 169.00 (167.25–182.00) 173.00 (165.00–180.00) 0.835 HR (bat/min.) mean ± SD
0.002 BSA (kg/m2 ) mean ± SD
0.432 LVIDs (cm) median (25–75) percentile 3.30 (2.90–3.70) 3.60 (3.05–4.00) 3.30 (2.90–3.70) 0.000 LVIDd (cm) median (25–75) percentile 5.00 (4.70–5.40) 5.00 (4.68–5.50) 5.00 (4.70–5.40) 0.617 IVSd (cm) mean ± SD
0.531 PLWd (cm) median (25–75) percentile 1.20 (1.10–1.30) 1.15 (1.00–1.20) 1.20 (1.10–1.30) 0.087 LA (cm) median (25–75) percentile 3.70 (3.40–3.90) 3.80 (3.40–4.30) 3.70 (3.40–3.90) 0.043 RV (cm) median (25–75) percentile 2.20 (2.00–2.40) 2.20 (2.00–2.53) 2.00 (1.80–2.00) 0.071 AO (cm) median (25–75) percentile 3.40 (3.20–3.60) 3.30 (3.10–3.50) 3.40 (3.20–3.60) 0.307 AOvs (cm) median (25–75) percentile 2.00 (1.80–2.00) 1.80 (1.60–2.00) 2.00 (1.80–2.00) <0.0005 EDVLV (mL) median (25–75) percentile 99.00 (85.00–121.00) 109 (80.50–133.50) 99.00 (85–120.88) 0.379 EDVLVI (mL/m2 ) mean ± SD
0.391 ESVLV (mL) median (25–75) percentile 47.00 (38.00–62.00) 65 (46.25–85.25) 47 (37–61) <0.0005 ESVLVI (mL/m2 ) median (25–75) percentile 23.56 (18.37–31.96) 48.21 (30.85–107.84) 23.41 (18.36–31.88) 0.021 SVLV (mL) median (25–75) percentile 50.00 (43.00–60.00) 40 (30–48.50) 51 (43–60) <0.0005 SVLVI (mL/m2 ) mean ± SD
0.204 LVEF (%) median (25–75) percentile 52.00 (45.00–57.00) 38 (28–47) 52 (45–58) <0.0005 CO (L/min.) mean ± SD
0.865 LVOTD (cm) median (25–75) percentile 2.00 (1.90–2.10) 1.90 (1.70–2.00) 2.00 (1.90–2.10) 0.006 LAab (cm) median (25–75) percentile 5.40 (5.00–5.70) 5.55 (4.90–6.20) 5.40 (5.00–5.70) 0.125 LAII (cm) median (25–75) percentile 3.90 (3.60–4.30) 4.30 (3.90–4.70) 3.90 (3.60–4.30) <0.0005 RAab (cm) median (25–75) percentile 4.80 (4.40–5.20) 5.05 (4.57–5.70) 4.80 (4.40–5.10) 0.008 RAII (cm) median (25–75) percentile 3.40 (3.10–3.70) 3.70 (3.30–4.35) 3.40 (3.10–3.70) <0.0005 AOmaxPG (mmHg) median (25–75) percentile 6.90 (5.20–9.30) 5.9 (4.4–8.8) 6.9 (5.20–9.30) 0.008 AOmeanPG (mmHg) median (25–75) percentile 3.60 (2.70–4.90) 3.10 (2.35–5.20) 3.60 (2.70–4.90) 0.086 AOVTI (cm) median (25–75) percentile 25.10 (21.00–30.00) 22.00 (15.00–29.50) 25.60 (21.20–30.00) 0.001 AVA (cm2 ) mean ± SD
<0.0005 AscAO (cm) median (25–75) percentile 3.70 (3.40–3.90) 3.70 (3.50–3.90) 3.70 (3.40–3.90) 0.680 DscAO (cm) mean ± SD
0.068 ArchAO (cm) mean ± SD
0.218 MADd (cm) median (25–75) percentile 3.10 (2.90–3.30) 3.20 (3.00–3.40) 3.10 (2.90–3.30) 0.078 MAAd (cm) median (25–75) percentile 7.54 (6.60–8.55) 8.04 (7.06–9.07) 7.54 (6.60–8.55) 0.043 MVA (cm2 ) mean ± SD
0.056 MVmaxPG (mmHg) median (25–75) percentile 3.60 (2.70–4.80) 3.80 (2.60–6.05) 3.60 (2.70–4.80) 0.253 MVmeanPG (mmHg) median (25–75) percentile 1.50 (1.02–2.00) 1.80 (1.10–2.50) 1.50 (1.00–2.00) 0.044 MVVTI (cm) median (25–75) percentile 23.00 (18.78–28.00) 19.00 (14.75–26.00) 23.50 (19.00–28.00) <0.0005 Emv (cm/sec.) median (25–75) percentile 0.80 (0.60–0.90) 1.00 (0.70–1.05) 0.70 (0.50–0.90) 0.017 Amv (cm/sec.) median (25–75) percentile 0.70 (0.60–0.90) 0.55 (0.38–0.83) 0.70 (0.60–0.90) 0.109 Emv/Amv median (25–75) percentile 1.00 (0.70–1.30) 1.55 (1.17–2.18) 0.95 (0.70–1.30) 0.028 MV Dct. (msec.) mean ± SD
0.429 RVd (cm) mean ± SD
0.437 RVs (cm) mean ± SD
0.045 RVSP (mmHg) median (25–75) percentile 33.00 (26.00–39.00) 38.00 (31.00–45.00) 33.00 (26.00–39.00) <0.0005 TrcPA (cm) median (25–75) percentile 2.10 (1.90–2.20) 2.00 (1.90–2.15) 2.10 (1.90–2.20) 0.367 PAmaxPG (mmHg) median (25–75) percentile 3.50 (2.70–4.80) 2.80 (1.73–4.45) 3.50 (2.70–4.80) 0.042 PAmeanPG (mmHg) median (25–75) percentile 1.70 (1.21–2.40) 1.15 (0.63–2.15) 1.80 (1.30–2.40) 0.010 PAVTI (cm) median (25–75) percentile 18.55 (15.93–22.00) 11.60 (7.25–18.23) 18.95 (16.00–22.00) <0.0005