Case Report

Dilatation of the Great Arteries in an Infant with Marfan Syndrome and Ventricular Septal Defect

Table 1

Aortic root diameters and pulmonary artery diameters during followup.

Age
(yr)
Height
cm (SDS)
Weight
(SDS)
BSA
(m2)
Aortic root
mm ( 𝑧 -score)
PV
mm ( 𝑧 -score)
MPA
mm ( 𝑧 -score)

0.775.0 (+1.5)5.5 (<−2.5)0.3422.0 (+8.6)22.0 (+6.2)27.5 (+8)
0.875.1 (+1.5)5.6 (<−2.5)0.3423.4 (+9.2)17.4 (+4.0)21.2 (+6)
3.7114.7 (>+2.5)16.0 (<−2.5)0.7332.3 (+8.4)20.0 (+1.9)21.0 (+2)
5.7129.0 (+2.5)18.0 (<−2.5)0.8338.7 (+9.9)19.0 (+0.9)19.1 (+1)

BSA: body surface area; PV: pulmonary valve; MPA: main pulmonary artery. 𝑧 -score according to Daubeney ([1], 284/id).