Pleuroparenchymal Fibroelastosis: A New Entity within the Spectrum of Rare Idiopathic Interstitial Pneumonias

Figure 9

Surgical lung biopsy of the right upper lobe of Case  2. (a) The alveolar structures are completely obliterated due to accumulation of elastotic material in the wall. HE 100x. (b) At higher magnification, the presence of a very small lymphocytic infiltration is showed. (c) Using the Van Gieson stain, the elastotic content of the wall is observed and the alveolar lumen is replaced by connective tissue. (d) Using autofluorescence, the presence of numerous elastic fibbers is observed in the same field of Figure 9(b).

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